Aortic root reconstruction in a nine-year-old child: a case report

J Heart Valve Dis. 2009 Mar;18(2):220-2.


Aortic root dilatation is present by the age of five years in approximately 35% of patients suffering from Marfan syndrome. However, children rarely undergo surgery for aortic aneurysm and aortic regurgitation during their first decade of life. A nine-year-old boy, who presented with severe aortic regurgitation associated with a 76.8 mm aneurysm of the ascending aorta, underwent a Bentall procedure. Since the aortic annulus was markedly dilated and the cusps were structurally abnormal, the aortic valve was not spared.

Publication types

  • Case Reports

MeSH terms

  • Aorta / surgery*
  • Aortic Aneurysm / surgery
  • Aortic Valve Insufficiency / etiology
  • Aortic Valve Insufficiency / surgery
  • Aortography
  • Child
  • Dilatation, Pathologic / surgery
  • Heart Valve Prosthesis
  • Humans
  • Male
  • Marfan Syndrome / surgery*