Spontaneous cervical extradural hematoma in a cutaneo-meningospinal angiomatosis (Cobb syndrome): case report

J Neurosurg Sci. 2009 Jun;53(2):59-61.


Spontaneous spinal extradural hematoma is a rare clinical entity, commonly associated with coagulopathies, tumours or vascular malformations. They are often a neurosurgical emergency, therefore prompt diagnosis and early treatment are necessary. The Cobb syndrome is a neurocutaneous syndrome in which there are metameric vascular skin nevus and spinal arteriovenous malformation. The authors report the case of a 52-year-old woman with acute cervical myelopathy and a cervical cutaneous hemangioma on clinical examination. It is stressed the importance of clinical suspicion of cutaneo-meningospinal angiomatosis based on a spinal cord syndrome in the presence of a vascular skin nevus of the same metameric level.

Publication types

  • Case Reports

MeSH terms

  • Angiomatosis / complications*
  • Angiomatosis / pathology
  • Angiomatosis / surgery
  • Arteriovenous Malformations / complications*
  • Arteriovenous Malformations / pathology
  • Arteriovenous Malformations / surgery
  • Female
  • Hematoma, Epidural, Cranial / etiology*
  • Hematoma, Epidural, Cranial / pathology
  • Hematoma, Epidural, Cranial / surgery
  • Humans
  • Magnetic Resonance Imaging
  • Middle Aged
  • Nevus / complications*
  • Nevus / pathology
  • Nevus / surgery
  • Skin Neoplasms / complications*
  • Skin Neoplasms / pathology
  • Skin Neoplasms / surgery