Mitochondrial abnormalities drive cell death in Wolfram syndrome 2

Cell Res. 2009 Aug;19(8):922-3. doi: 10.1038/cr.2009.94.
No abstract available

MeSH terms

  • Aging, Premature / genetics*
  • Animals
  • Autophagy-Related Proteins
  • Carrier Proteins / genetics*
  • Carrier Proteins / metabolism
  • Cell Death
  • DNA Polymerase gamma
  • DNA-Directed DNA Polymerase / deficiency
  • DNA-Directed DNA Polymerase / genetics
  • DNA-Directed DNA Polymerase / metabolism
  • Membrane Proteins / genetics
  • Membrane Proteins / metabolism
  • Mice
  • Mitochondria / genetics*
  • Mitochondria / metabolism
  • Nerve Tissue Proteins / deficiency
  • Nerve Tissue Proteins / genetics*
  • Nerve Tissue Proteins / metabolism
  • Wolfram Syndrome / genetics*
  • Wolfram Syndrome / metabolism

Substances

  • Autophagy-Related Proteins
  • Carrier Proteins
  • Membrane Proteins
  • Nerve Tissue Proteins
  • Noxp70 protein, mouse
  • wolframin protein
  • DNA Polymerase gamma
  • DNA-Directed DNA Polymerase
  • Polg protein, mouse