Recurrent ventricular tachycardia in patient with Friedreich's ataxia in the absence of clinical myocardial disease

Pacing Clin Electrophysiol. 2010 Jan;33(1):109-12. doi: 10.1111/j.1540-8159.2009.02528.x. Epub 2009 Sep 10.


We report a 33-year-old man with recurrent loss of consciousness due to ventricular tachyarrhythmia with a history of Friedreich's ataxia. The patient's symptom was improved after implantation of a single-lead implantable cardiac defibrillator. The clinical, genetic, echocardiographic, and electrocardiographic features are discussed in brief.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Defibrillators, Implantable
  • Friedreich Ataxia / complications*
  • Humans
  • Male
  • Recurrence
  • Tachycardia, Ventricular / complications*
  • Tachycardia, Ventricular / therapy