Primary extraosseous ewing sarcoma of the kidney with level III inferior vena cava thrombus

Clin Genitourin Cancer. 2009 Oct;7(3):E95-7. doi: 10.3816/CGC.2009.n.032.


Ewing sarcoma typically presents as a skeletal-based tumor, with rare instances of peripheral primitive neuroectodermal tumor (PNET) arising in the soft tissues. Few examples of organ-based PNETs have been previously described in the literature. These tumors are exceedingly rare as a primary renal neoplasm. To our knowledge, this is the first report documenting a primary extraskeletal Ewing sarcoma of the kidney with thrombus extending into the intrahepatic inferior vena cava thrombus (level III).

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Humans
  • Kidney Neoplasms / diagnosis*
  • Kidney Neoplasms / diagnostic imaging
  • Kidney Neoplasms / pathology
  • Male
  • Neuroectodermal Tumors, Primitive, Peripheral / diagnostic imaging
  • Neuroectodermal Tumors, Primitive, Peripheral / pathology
  • Sarcoma, Ewing / diagnosis*
  • Sarcoma, Ewing / diagnostic imaging
  • Sarcoma, Ewing / pathology
  • Tomography, X-Ray Computed
  • Vena Cava, Inferior*
  • Venous Thrombosis / diagnostic imaging