Hyperargininemia: intellectual and motor improvement related to changes in biochemical data

J Pediatr. 1991 Mar;118(3):420-4. doi: 10.1016/s0022-3476(05)82161-4.
No abstract available

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Metabolism, Inborn Errors / blood
  • Amino Acid Metabolism, Inborn Errors / cerebrospinal fluid
  • Amino Acid Metabolism, Inborn Errors / diet therapy*
  • Amino Acid Metabolism, Inborn Errors / psychology
  • Arginine / blood*
  • Arginine / cerebrospinal fluid
  • Child
  • Female
  • Guanidines / blood
  • Guanidines / cerebrospinal fluid
  • Humans
  • Intelligence*
  • Motor Skills*
  • Muscle Spasticity / prevention & control
  • Muscles / physiopathology
  • Psychomotor Performance

Substances

  • Guanidines
  • alpha-keto-delta-guanidinovaleric acid
  • Arginine