Modified encephaloduroarteriosynangiosis as a surgical treatment of childhood moyamoya disease: report of five cases

J Child Neurol. 1991 Jan;6(1):24-31. doi: 10.1177/088307389100600105.


Moyamoya disease is an idiopathic disorder characterized by progressive occlusion of the internal carotid and anterior and middle cerebral arteries, with formation of an extensive abnormal collateral circulation at the base of the brain. Many neurosurgical procedures have been designed to bypass these occluded vessels. The results of one of these procedures, modified encephaloduroarteriosynangiosis was reviewed in five children followed for 3 1/2 to 19 1/2 years. Modified encephaloduroarteriosynangiosis performed unilaterally in one and bilaterally in four of the children, appeared to halt neurologic deterioration, despite angiographic progression, in four of the five children.

Publication types

  • Case Reports

MeSH terms

  • Brain Ischemia / diagnostic imaging
  • Brain Ischemia / surgery*
  • Carotid Artery Diseases / diagnostic imaging
  • Carotid Artery Diseases / surgery
  • Cerebral Angiography
  • Cerebral Revascularization / methods*
  • Child
  • Child, Preschool
  • Collateral Circulation / physiology
  • Female
  • Follow-Up Studies
  • Humans
  • Infant
  • Ischemic Attack, Transient / diagnostic imaging
  • Ischemic Attack, Transient / surgery
  • Male
  • Moyamoya Disease / diagnostic imaging
  • Moyamoya Disease / surgery*
  • Postoperative Complications / diagnostic imaging
  • Postoperative Complications / surgery
  • Reoperation