Tapia syndrome was first described by Antonio Garcia Tapia in 1904. Then, he believed that the existing lesion, resulting in some neurologic symptoms, was outside the central nervous system. Nowadays, this syndrome is characterized by the unilateral paralysis of the tongue and the vocal cord. Possible cause of this disorder is injury to the 10th and 12th cranial nerves without involvement of the pharyngeal branches of the 10th nerve. We present a patient with Tapia syndrome together with its treatment and new classification.