Bilateral papillary cystadenoma of the mesosalpinx: a rare manifestation of Von Hippel-Lindau disease

Arch Gynecol Obstet. 2010 Sep;282(3):343-6. doi: 10.1007/s00404-010-1386-4. Epub 2010 Feb 16.

Abstract

We report a rare case of a woman with bilateral papillary cystadenomata of the broad ligament with von Hippel-Lindau disease (VHL) (other manifestations: capillary hemangioblastomas of the spinal cord). Patient surveillance is important, because in the course of VHL-associated tumors malignant lesions may arise that are relevant for the prognosis.

Publication types

  • Case Reports

MeSH terms

  • Cystadenoma, Papillary / etiology*
  • Cystadenoma, Papillary / genetics
  • Cystadenoma, Papillary / pathology
  • Fallopian Tube Neoplasms / etiology*
  • Fallopian Tube Neoplasms / genetics
  • Fallopian Tube Neoplasms / pathology
  • Female
  • Hemangioblastoma / etiology*
  • Humans
  • Point Mutation
  • Spinal Cord Neoplasms / etiology*
  • Thoracic Vertebrae
  • Von Hippel-Lindau Tumor Suppressor Protein / genetics
  • Young Adult
  • von Hippel-Lindau Disease / complications*
  • von Hippel-Lindau Disease / diagnosis*
  • von Hippel-Lindau Disease / genetics

Substances

  • Von Hippel-Lindau Tumor Suppressor Protein
  • VHL protein, human