Glycoprotein Ib bioassays. Activity levels in Bernard-Soulier syndrome and in stored blood bank platelets

Arch Pathol Lab Med. 1991 May;115(5):488-93.

Abstract

Glycoprotein Ib (GP-Ib) is a major platelet receptor protein concerned with von Willebrand-factor binding, platelet agglutination, and platelet adhesion, and it is required for normal hemostasis. By the use of botrocetin (venom coagglutinin), both quantitative and semiquantitative assays for GP-Ib activity were developed. The latter assay uses limiting dilutions of botrocetin as a measure of GP-Ib activity. Platelets, stored up to 23 days under blood bank conditions, were assayed by the limiting dilution test. Values of GP-Ib were progressively diminished after 9 to 10 days of storage, reaching levels of less than 10% at 23 days. Platelets from a subject with Bernard-Soulier syndrome showed less than 10% GP-Ib activity. These assays appear to be a specific measure of functional GP-Ib activity, and, when combined with GP-Ib antigen measurement by other methods, they provide a means for further characterizing GP-Ib abnormalities.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Bernard-Soulier Syndrome / blood*
  • Blood Banks*
  • Blood Platelets / metabolism*
  • Blood Preservation*
  • Crotalid Venoms
  • Hemagglutinins
  • Humans
  • Indicator Dilution Techniques
  • Platelet Membrane Glycoproteins / analysis*
  • Time Factors

Substances

  • Crotalid Venoms
  • Hemagglutinins
  • Platelet Membrane Glycoproteins
  • botrocetin