Case report: Clinical, histological and ultrastructural characterization of type II dentinogenesis imperfecta

Eur Arch Paediatr Dent. 2010 Dec;11(6):306-9. doi: 10.1007/BF03262769.


Background: Type II dentinogenesis imperfecta (DGIII) is an autosomal dominant dental development anomaly that affects both the primary and permanent dentition.

Case report: This case report describes the clinical, radiographic and morphological characteristics of the teeth of a seven-year-old child with DGI-II determined by optical microscopy and scanning electron microscopy.

Treatment: This consisted of extraction of the primary teeth with periapical lesions due to the advanced state of tooth resorption. Aesthetic restorations were performed on the mandibular anterior teeth and occlusal fissure sealants were applied to erupting teeth. A removable partial upper denture was made in order to return anterior aesthetic function and to aid mastication and speech.

Follow up: The child was examined at 3 month intervals. Over the following 3 years the prosthesis was replaced due to facial growth and fluoride was applied at each follow-up visit to all teeth. The patient remains in follow up and management.

Conclusion: Individuals with DGI-II must not neglect their dental health. Early diagnosis, professional advice and treatment with periodic follow-up can help improve the quality of life of such patients.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Child
  • Cuspid / abnormalities
  • Dental Enamel / pathology
  • Dental Enamel / ultrastructure
  • Dentin / pathology
  • Dentin / ultrastructure
  • Dentinogenesis Imperfecta / classification*
  • Dentinogenesis Imperfecta / pathology
  • Denture Design
  • Denture, Partial, Removable
  • Follow-Up Studies
  • Humans
  • Incisor / abnormalities
  • Male
  • Microscopy, Electron, Scanning
  • Periapical Diseases / therapy
  • Tooth Extraction
  • Tooth Resorption / therapy
  • Tooth, Deciduous / abnormalities