There are several thyroid gland developmental anomalies such as presence of a pyramidal lobe, absence of the lateral lobes, absence of the isthmus or incomplete isthmus, and significantly asymmetric lateral lobes. The absence or agenesis of the isthmus is a rare condition (1%). In this report, we present a case with Hashimoto thyroiditis and thyroid gland anomalies that consist of thyroglossal duct remnant and absence of the isthmus. Furthermore, an anomaly in the parathyroid gland location and morphologic anomaly as a cystic parathyroid gland were seen in our case.