Platelet secretion defect in patients with familial hemophagocytic lymphohistiocytosis type 5 (FHL-5)

Blood. 2010 Dec 23;116(26):6148-50. doi: 10.1182/blood-2010-08-302943.
No abstract available

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Blood Platelet Disorders / etiology*
  • Blood Platelets / drug effects
  • Blood Platelets / metabolism*
  • Flow Cytometry
  • Hemostatics / pharmacology
  • Humans
  • Lymphohistiocytosis, Hemophagocytic / complications
  • Lymphohistiocytosis, Hemophagocytic / genetics
  • Platelet Aggregation / drug effects
  • Thrombin / pharmacology

Substances

  • Hemostatics
  • Thrombin