Repair of ascending aortic aneurysm in a patient with arterial tortuosity syndrome

Interact Cardiovasc Thorac Surg. 2011 Jun;12(6):1051-3. doi: 10.1510/icvts.2010.265082. Epub 2011 Mar 25.

Abstract

Arterial tortuosity syndrome (ATS) is a rare connective tissue disease characterized by aneurysms and stenosis of large elastic arteries. In this case report, we present the case of an eight-year-old with ATS who underwent successful hemi-arch and ascending aortic replacement with tube graft.

Publication types

  • Case Reports

MeSH terms

  • Aortic Aneurysm / diagnostic imaging
  • Aortic Aneurysm / etiology
  • Aortic Aneurysm / surgery*
  • Aortography / methods
  • Blood Vessel Prosthesis Implantation*
  • Child
  • Connective Tissue Diseases / complications*
  • Connective Tissue Diseases / genetics
  • Humans
  • Male
  • Tomography, X-Ray Computed
  • Treatment Outcome