Structural basis of thrombin-mediated factor V activation: the Glu666-Glu672 sequence is critical for processing at the heavy chain-B domain junction

Blood. 2011 Jun 30;117(26):7164-73. doi: 10.1182/blood-2010-10-315309. Epub 2011 May 9.

Abstract

Thrombin-catalyzed activation of coagulation factor V (FV) is an essential positive feedback reaction within the blood clotting system. Efficient processing at the N- (Arg(709)-Ser(710)) and C-terminal activation cleavage sites (Arg(1545)-Ser(1546)) requires initial substrate interactions with 2 clusters of positively charged residues on the proteinase surface, exosites I and II. We addressed the mechanism of activation of human factor V (FV) using peptides that cover the entire acidic regions preceding these cleavage sites, FV (657-709)/ (FVa2) and FV(1481-1545)/(FVa3). FVa2 appears to interact mostly with exosite I, while both exosites are involved in interactions with the C-terminal linker. The 1.7-Å crystal structure of irreversibly inhibited thrombin bound to FVa2 unambiguously reveals docking of FV residues Glu(666)-Glu(672) to exosite I. These findings were confirmed in a second, medium-resolution structure of FVa2 bound to the benzamidine-inhibited proteinase. Our results suggest that the acidic A2-B domain linker is involved in major interactions with thrombin during cofactor activation, with its more N-terminal hirudin-like sequence playing a critical role. Modeling experiments indicate that FVa2, and likely also FVa3, wrap around thrombin in productive thrombin·FV complexes that cover a large surface of the activator to engage the active site.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Chloromethyl Ketones / chemistry
  • Amino Acid Chloromethyl Ketones / pharmacology
  • Amino Acid Sequence
  • Antithrombins / chemistry
  • Antithrombins / pharmacology
  • Benzamidines / chemistry
  • Benzamidines / pharmacology
  • Biocatalysis
  • Catalytic Domain
  • Crystallography, X-Ray
  • Enzyme Activation
  • Enzymes, Immobilized / antagonists & inhibitors
  • Enzymes, Immobilized / chemistry
  • Enzymes, Immobilized / metabolism
  • Factor V / chemistry*
  • Factor V / genetics
  • Factor V / metabolism*
  • Factor Va / chemistry
  • Factor Va / genetics
  • Factor Va / metabolism
  • Humans
  • Kinetics
  • Models, Molecular
  • Peptide Fragments / chemistry
  • Peptide Fragments / genetics
  • Peptide Fragments / metabolism
  • Protein Conformation
  • Protein Interaction Domains and Motifs
  • Recombinant Proteins / chemistry
  • Recombinant Proteins / metabolism
  • Spectrometry, Fluorescence
  • Surface Plasmon Resonance
  • Surface Properties
  • Thrombin / antagonists & inhibitors
  • Thrombin / chemistry*
  • Thrombin / metabolism*

Substances

  • Amino Acid Chloromethyl Ketones
  • Antithrombins
  • Benzamidines
  • Enzymes, Immobilized
  • Peptide Fragments
  • Recombinant Proteins
  • Factor Va
  • Factor V
  • Thrombin
  • benzamidine
  • phenylalanyl-prolyl-arginine-chloromethyl ketone

Associated data

  • PDB/3P6Z
  • PDB/3P70