Purpose: To report a case of frosted branch angiitis (FBA) secondary to neuro-Behçet.
Methods: Description, diagnosis, angiogram imaging and follow-up of a 28-year-old female with FBA.
Results: 'Frosted branch angiitis' is a clinical term applied to three conditions: infiltration of vessels by malignant cells, and sheathing of vessels either secondary to an active disorder or subsequently to a previous inflammatory disease. Our patient's history of two optic neuropathies and the lack of demyelinating signs in neuroimaging made us consider FBA in the context of neuro-Behçet.
Conclusion: Recognition of the category of FBA from the clinical signs is essential to establish the correct diagnosis and prescribe the appropriate treatment.
Keywords: Behçet's disease; Frosted branch angiitis; Neuro-Behçet; Uveitis.