Abstract
We review the case of an adolescent who presented with flank pain, fatigue and a discrete nonfunctioning adrenal lesion which was found to be an adrenal Ewing sarcoma/primitive neuroectodermal tumor (ES/PNET). The patient was treated with a minimally invasive adrenalectomy as a component of multimodal therapy, including seven courses of chemotherapy and whole abdominal radiation. She is currently disease free 14 months after the operation and 3 months off therapy.
Copyright © 2011 Wiley-Liss, Inc.
MeSH terms
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Adolescent
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Adrenal Cortex Neoplasms / pathology*
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Adrenal Cortex Neoplasms / therapy
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Adrenalectomy
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Antineoplastic Combined Chemotherapy Protocols / administration & dosage
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Combined Modality Therapy
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Cyclophosphamide / administration & dosage
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Doxorubicin / administration & dosage
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Etoposide / administration & dosage
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Female
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Humans
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Ifosfamide / administration & dosage
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Neuroectodermal Tumors, Primitive, Peripheral / pathology*
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Neuroectodermal Tumors, Primitive, Peripheral / therapy
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Radiotherapy
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Sarcoma, Ewing / pathology*
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Sarcoma, Ewing / therapy
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Vincristine / administration & dosage
Substances
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Vincristine
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Etoposide
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Doxorubicin
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Cyclophosphamide
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Ifosfamide