Long-QT syndrome

Cardiol Rev. 2011 Sep-Oct;19(5):217-25. doi: 10.1097/CRD.0b013e3182203504.

Abstract

Acquired and hereditary long-QT syndromes are important causes of sudden cardiac death. Both categories are characterized by abnormally prolonged cardiac repolarization arising from a complex interaction between genetic and environmental factors. This produces a potentially dangerous substrate for polymorphic ventricular tachycardia and sudden cardiac death. In this review, the pathophysiologic, diagnostic, and prognostic features of long-QT syndromes, as well as recommendations regarding therapy, are reviewed.

Publication types

  • Review

MeSH terms

  • Action Potentials
  • Death, Sudden, Cardiac / etiology
  • Electrocardiography
  • Humans
  • Long QT Syndrome / diagnosis
  • Long QT Syndrome / genetics
  • Long QT Syndrome / physiopathology*
  • Long QT Syndrome / therapy
  • Prognosis
  • Torsades de Pointes / physiopathology