New phenotype with generalized platyspondyly, large mandible, hypoplastic teeth, strabismus, hyperopia and low cholesterol levels

Genet Couns. 2011;22(2):129-34.

Abstract

A sporadic, adult male patient with generalized platyspondyly, large mandible, hypoplastic teeth, strabismus, and low serum cholesterol levels is presented. Some of the patient's features resemble brachyolmia, Spondylo-epiphyseal dysplasia tarda, Kenny-Caffey and Stickler syndromes. Based on literature review, possible diagnoses are discussed. In conclusion, this patient can have a variant of brachyolmia or Spondylo-epiphyseal dysplasia tarda. However, we cannot exclude that this constellation of clinical features may represent a new syndrome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Cholesterol / blood*
  • Diagnosis, Differential
  • Humans
  • Hyperopia / diagnosis*
  • Hyperopia / pathology
  • Male
  • Mandible / pathology*
  • Osteochondrodysplasias / diagnosis*
  • Osteochondrodysplasias / pathology
  • Phenotype
  • Strabismus / diagnosis*
  • Strabismus / pathology
  • Syndrome
  • Tooth / pathology*

Substances

  • Cholesterol

Supplementary concepts

  • Brachyolmia