Angiokeratomas are relatively rare vascular lesions characterized by ectasias of the papillary dermal blood vessels with secondary epidermal changes in the form of acanthosis and/or hyperkeratosis. Amongst the several variants of angiokeratomas, angiokeratoma circumscriptum is the least common one. Angiokeratoma circumscriptum naeviforme (ACN) is a still rarer type of angiokeratoma, which is typically seen at birth. We report here a case of linear, unilateral, verrucous plaques on the leg of a young man, diagnosed as ACN.