Electrocardiographic abnormalities in patients with myotonic dystrophy

West J Med. 1990 Jul;153(1):24-7.


In examining the incidence and progression of electrocardiographic abnormalities in 45 patients with myotonic dystrophy, 26 (58%) of whom at entry had at least 1 electrocardiographic abnormality, we found conduction abnormalities in 17 (38%). In 21 patients (47%), new abnormalities developed during follow-up (mean, 4.6 years). The overall incidence of electrocardiographic abnormalities increased to 78%, and the incidence of conduction defects increased to 62%. Second-degree or complete atrioventricular block did not develop in any of the patients. Pseudoinfarction patterns were common at entry and during follow-up and were not correlated with evidence of clinical coronary artery disease. There was no correlation between the presence of electrocardiographic abnormalities and apparent disease severity.

Publication types

  • Review

MeSH terms

  • Adolescent
  • Adult
  • Arrhythmias, Cardiac / physiopathology*
  • Child
  • Electrocardiography*
  • Female
  • Follow-Up Studies
  • Heart Block / physiopathology
  • Heart Conduction System / physiopathology
  • Humans
  • Male
  • Middle Aged
  • Myotonic Dystrophy / physiopathology*