[Pyoderma gangrenosum and Behçet's disease: a study of two pediatric cases]

Arch Pediatr. 2011 Dec;18(12):1320-3. doi: 10.1016/j.arcped.2011.09.007. Epub 2011 Oct 24.
[Article in French]

Abstract

Pyoderma gangrenosum is a rare neutrophilic dermatosis that affects 4% of children. It is characterized by its association in half of the cases with an underlying disease. The association with Behçet's disease is exceptional and may have a very poor prognosis. We report 2 pediatric observations with fatal outcome.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adolescent
  • Behcet Syndrome / complications*
  • Behcet Syndrome / diagnosis
  • Behcet Syndrome / drug therapy
  • Behcet Syndrome / genetics
  • Child
  • Dermatologic Agents / therapeutic use
  • Drug Therapy, Combination
  • Fatal Outcome
  • Female
  • Glucocorticoids / therapeutic use
  • Humans
  • Male
  • Pedigree
  • Prednisone / therapeutic use
  • Prognosis
  • Pulmonary Edema / diagnosis
  • Pulmonary Edema / etiology
  • Pulmonary Edema / therapy
  • Pyoderma Gangrenosum / complications*
  • Pyoderma Gangrenosum / diagnosis
  • Pyoderma Gangrenosum / drug therapy
  • Recurrence
  • Thalidomide / therapeutic use

Substances

  • Dermatologic Agents
  • Glucocorticoids
  • Thalidomide
  • Prednisone