Abstract
Pyoderma gangrenosum is a rare neutrophilic dermatosis that affects 4% of children. It is characterized by its association in half of the cases with an underlying disease. The association with Behçet's disease is exceptional and may have a very poor prognosis. We report 2 pediatric observations with fatal outcome.
Copyright © 2011 Elsevier Masson SAS. All rights reserved.
Publication types
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Case Reports
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English Abstract
MeSH terms
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Adolescent
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Behcet Syndrome / complications*
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Behcet Syndrome / diagnosis
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Behcet Syndrome / drug therapy
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Behcet Syndrome / genetics
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Child
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Dermatologic Agents / therapeutic use
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Drug Therapy, Combination
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Fatal Outcome
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Female
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Glucocorticoids / therapeutic use
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Humans
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Male
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Pedigree
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Prednisone / therapeutic use
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Prognosis
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Pulmonary Edema / diagnosis
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Pulmonary Edema / etiology
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Pulmonary Edema / therapy
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Pyoderma Gangrenosum / complications*
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Pyoderma Gangrenosum / diagnosis
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Pyoderma Gangrenosum / drug therapy
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Recurrence
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Thalidomide / therapeutic use
Substances
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Dermatologic Agents
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Glucocorticoids
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Thalidomide
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Prednisone