Epidermodysplasia verruciformis: clinical presentation with varied forms of lesions

An Bras Dermatol. 2011 Jul-Aug;86(4 Suppl 1):S57-60. doi: 10.1590/s0365-05962011000700014.
[Article in English, Portuguese]

Abstract

Epidermodysplasia verruciformis is a rare inherited skin disorder spread by HPV, with cases linked to chromosome X. It is characterized by hypo- or hyper-pigmented macular lesions, pityriasis versicolor-like lesions and an early tendency to develop skin malignancies. We present a case of epidermodysplasia verruciformis with a variety of lesions such as multiple plane warts, pityriasis versicolor-like lesions and aggressive squamous cell carcinoma on the face.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Carcinoma, Squamous Cell / pathology*
  • Carcinoma, Squamous Cell / virology
  • Epidermodysplasia Verruciformis / pathology*
  • Epidermodysplasia Verruciformis / virology
  • Female
  • Humans
  • Skin Neoplasms / pathology*
  • Skin Neoplasms / virology