Epidermodysplasia verruciformis: clinical presentation with varied forms of lesions
An Bras Dermatol. 2011 Jul-Aug;86(4 Suppl 1):S57-60.
doi: 10.1590/s0365-05962011000700014.
[Article in
English,
Portuguese]
Affiliation
- 1 Hospital Universitário Polyodoro Ernani de São Thiago, Universidade Federal de Santa Catarina, Florianópolis, SC, Brasil. naianabdesa@hotmail.com
Abstract
Epidermodysplasia verruciformis is a rare inherited skin disorder spread by HPV, with cases linked to chromosome X. It is characterized by hypo- or hyper-pigmented macular lesions, pityriasis versicolor-like lesions and an early tendency to develop skin malignancies. We present a case of epidermodysplasia verruciformis with a variety of lesions such as multiple plane warts, pityriasis versicolor-like lesions and aggressive squamous cell carcinoma on the face.
MeSH terms
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Adult
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Carcinoma, Squamous Cell / pathology*
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Carcinoma, Squamous Cell / virology
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Epidermodysplasia Verruciformis / pathology*
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Epidermodysplasia Verruciformis / virology
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Female
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Humans
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Skin Neoplasms / pathology*
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Skin Neoplasms / virology