A to Z of extraskeletal Ewing sarcoma family of tumors in adults: imaging features of primary disease, metastatic patterns, and treatment responses

AJR Am J Roentgenol. 2011 Dec;197(6):W1015-22. doi: 10.2214/AJR.11.6667.


Objective: Though classically thought of as an osseous-based sarcoma of children and adolescents, it is important to recognize that approximately 20% of all cases of Ewing sarcoma family of tumors (ESFT) occur in patients older than 18 years, often with extraskeletal disease. Understanding the specific imaging features, manners of presentation, and patterns of behavior of ESFT is therefore important in all settings.

Conclusion: This article presents the imaging findings of ESFT in the adult, with specific attention to extraskeletal manifestations.

Publication types

  • Review

MeSH terms

  • Adult
  • Contrast Media
  • Diagnostic Imaging*
  • Humans
  • Neuroectodermal Tumors, Primitive, Peripheral / diagnosis*
  • Neuroectodermal Tumors, Primitive, Peripheral / pathology
  • Neuroectodermal Tumors, Primitive, Peripheral / therapy
  • Sarcoma, Ewing / diagnosis*
  • Sarcoma, Ewing / pathology
  • Sarcoma, Ewing / therapy


  • Contrast Media