Prune belly syndrome

Pediatr Surg Int. 2012 Mar;28(3):219-28. doi: 10.1007/s00383-011-3046-6. Epub 2011 Dec 25.


The majority of paediatric surgeons will encounter a patient with prune belly syndrome (PBS) only a few times in their clinical practice. There have been many opposing views in the literature regarding the pathogenesis and management of this complex condition. A detailed review was conducted using PubMed to identify key publications involving PBS. This article discusses the evolution of our understanding of the pathogenesis and diagnosis of PBS, including its typical characteristics. We describe the management options available for bilateral intra-abdominal testes, the deficient abdominal wall, the dilated urinary system and examine the evidence base used to support the current approaches employed.

Publication types

  • Review

MeSH terms

  • Child
  • Diagnostic Imaging / methods*
  • Global Health
  • Humans
  • Incidence
  • Male
  • Plastic Surgery Procedures / methods*
  • Prune Belly Syndrome* / diagnosis
  • Prune Belly Syndrome* / epidemiology
  • Prune Belly Syndrome* / surgery