Slowly progressive Foix-Chavany-Marie syndrome as a precursor of a primary progressive aphasia

J Clin Neurosci. 2012 May;19(5):765-7. doi: 10.1016/j.jocn.2011.08.021. Epub 2012 Feb 8.

Abstract

Foix-Chavany-Marie syndrome (FCMS) is a rare neurological condition usually associated with bilateral ischemic lesions of the anterior frontoparietal operculum. Here, we present a patient with slowly progressive FCMS owing to focal brain atrophy who developed a language disorder similar to that seen in a primary progressive aphasia.

Publication types

  • Case Reports

MeSH terms

  • Aphasia, Primary Progressive / etiology
  • Aphasia, Primary Progressive / pathology*
  • Aphasia, Primary Progressive / physiopathology*
  • Apraxias / etiology
  • Apraxias / pathology
  • Apraxias / physiopathology
  • Deglutition Disorders / complications
  • Deglutition Disorders / etiology
  • Deglutition Disorders / pathology*
  • Deglutition Disorders / physiopathology*
  • Dysarthria / complications
  • Dysarthria / pathology*
  • Dysarthria / physiopathology*
  • Encephalomyelitis, Acute Disseminated / complications
  • Encephalomyelitis, Acute Disseminated / pathology*
  • Encephalomyelitis, Acute Disseminated / physiopathology*
  • Facial Paralysis / complications
  • Facial Paralysis / pathology*
  • Facial Paralysis / physiopathology*
  • Female
  • Frontotemporal Dementia / complications
  • Frontotemporal Dementia / pathology*
  • Frontotemporal Dementia / physiopathology*
  • Humans
  • Middle Aged
  • Movement Disorders / etiology
  • Movement Disorders / pathology
  • Movement Disorders / physiopathology

Supplementary concepts

  • Foix Chavany Marie syndrome