The birth of an individual with a blend of both male and female internal or external genitalia is known as an intersex condition. The incidence of genital anomalies is estimated to occur in 1 in 4,500 live births. Each intersex condition is determined by the external genital appearance, internal genital structures, and fertility potential. The main concept involved in the management of intersex is the establishment of an experienced multidisciplinary team. Management of intersex conditions is complex and involves a person's gender identity, gender role behavior, sexual orientation, sexual functioning, and psychological adjustment. This review will outline the management of intersex in the light of the latest research. We focus on diagnosis, surgical techniques, and the psychological aspects that are encountered in the management of intersex.