Pulmonary arterial hypertension with plexogenic arteriopathy in enzyme-substituted Gaucher disease

Histopathology. 2012 Aug;61(2):324-6. doi: 10.1111/j.1365-2559.2012.04261.x. Epub 2012 Jun 13.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Enzyme Replacement Therapy
  • Familial Primary Pulmonary Hypertension
  • Female
  • Gaucher Disease / classification
  • Gaucher Disease / complications*
  • Gaucher Disease / drug therapy*
  • Gaucher Disease / pathology
  • Glucosylceramidase / therapeutic use
  • Humans
  • Hypertension, Pulmonary / etiology*
  • Hypertension, Pulmonary / pathology
  • Hypertension, Pulmonary / therapy
  • Lung Transplantation
  • Middle Aged
  • Pulmonary Artery / pathology
  • Recombinant Proteins / therapeutic use

Substances

  • Recombinant Proteins
  • Glucosylceramidase
  • imiglucerase