Cofilin/Twinstar phosphorylation levels increase in response to impaired coenzyme a metabolism

PLoS One. 2012;7(8):e43145. doi: 10.1371/journal.pone.0043145. Epub 2012 Aug 17.

Abstract

Coenzyme A (CoA) is a pantothenic acid-derived metabolite essential for many fundamental cellular processes including energy, lipid and amino acid metabolism. Pantothenate kinase (PANK), which catalyses the first step in the conversion of pantothenic acid to CoA, has been associated with a rare neurodegenerative disorder PKAN. However, the consequences of impaired PANK activity are poorly understood. Here we use Drosophila and human neuronal cell cultures to show how PANK deficiency leads to abnormalities in F-actin organization. Cells with reduced PANK activity are characterized by abnormally high levels of phosphorylated cofilin, a conserved actin filament severing protein. The increased levels of phospho-cofilin coincide with morphological changes of PANK-deficient Drosophila S2 cells and human neuronal SHSY-5Y cells. The latter exhibit also markedly reduced ability to form neurites in culture--a process that is strongly dependent on actin remodeling. Our results reveal a novel and conserved link between a metabolic biosynthesis pathway, and regulation of cellular actin dynamics.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Actins / metabolism*
  • Animals
  • Cell Line, Tumor
  • Cells, Cultured
  • Coenzyme A / metabolism*
  • Drosophila / metabolism*
  • Drosophila Proteins / metabolism*
  • Humans
  • Immunoblotting
  • Microfilament Proteins / metabolism*
  • Microscopy, Fluorescence
  • Neurites / physiology
  • Neurons / metabolism*
  • Phosphorylation
  • Phosphotransferases (Alcohol Group Acceptor) / deficiency*
  • RNA Interference

Substances

  • Actins
  • Drosophila Proteins
  • Microfilament Proteins
  • tsr protein, Drosophila
  • Phosphotransferases (Alcohol Group Acceptor)
  • pantothenate kinase
  • Coenzyme A

Grants and funding

Dutch organization for scientific research (NWO) funded the described work in a VICI Grant to Ody Sibon. The funders had no role in study design, data collection and analysis, decision to publish, or preparation of the manuscript.