To our knowledge, this is the first case of vulvar leiomyosarcoma occurring during pregnancy to be reported. The neoplasm was resected immediately after a term vaginal delivery. A wide local excision of the vulva with bilateral superficial inguinal node sampling was performed 6 weeks post partum. Four previous cases of vulvar sarcoma occurring in pregnancy are reviewed. The need to perform biopsy of vulvar lesions during pregnancy is emphasized.