Cardiopulmonary exercise testing reveals onset of disease and response to treatment in a case of heritable pulmonary arterial hypertension

Pulm Circ. 2012 Jul;2(3):387-9. doi: 10.4103/2045-8932.101658.


Patients affected by pulmonary arterial hypertension (PAH) show a typical pattern of abnormalities on cardiopulmonary exercise testing (CPET). However, CPET is not routinely used as a screening method. We discuss a patient with hereditary PAH in whom CPET revealed onset of disease. Furthermore, we show that the abnormalities observed can improve in part by PAH-specific treatment.

Keywords: cardiopulmonary exercise testing; pulmonary hypertension; treatment response.

Publication types

  • Case Reports