Rosai-Dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, is a benign disorder of histiocyte proliferation that usually affects the lymph nodes. Cutaneous Rosai-Dorfman disease (CRDD) is a rare extranodal variant that is strictly limited to the skin. We report a patient with CRDD of the trunk. A brief review of the literature of CRDD also is provided.