Rapid progressive bilateral hearing loss due to granulomatous otitis media in Lyme disease

Am J Otolaryngol. 2013 May-Jun;34(3):245-7. doi: 10.1016/j.amjoto.2012.11.009. Epub 2013 Jan 11.

Abstract

We report on a patient with Lyme disease who presented with chronic bilateral otitis media and cranial neuropathy with rapid progressive hearing loss. After ceftriaxone and high-dose intravenous immunoglobulins, the disease was controlled only with methylprednisolone and cyclophosphamide. The relationship between Lyme disease and granulomatous vasculitis is discussed. Lyme disease should be kept in mind in the differential diagnosis of various otolaryngological and neurological presentations.

Publication types

  • Case Reports

MeSH terms

  • Anti-Inflammatory Agents / administration & dosage
  • Chronic Disease
  • Cranial Nerve Diseases / complications
  • Cyclophosphamide / administration & dosage
  • Disease Progression
  • Fatal Outcome
  • Granuloma / complications*
  • Hearing Loss, Bilateral / diagnosis
  • Hearing Loss, Bilateral / etiology*
  • Humans
  • Lyme Disease / complications*
  • Male
  • Methylprednisolone / administration & dosage
  • Middle Aged
  • Myocardial Infarction / complications
  • Otitis Media / complications*
  • Otoscopy
  • Tympanic Membrane Perforation / complications
  • Vasculitis / complications

Substances

  • Anti-Inflammatory Agents
  • Cyclophosphamide
  • Methylprednisolone