Giant cellulitis-like Sweet Syndrome, a new variant of neutrophilic dermatosis

JAMA Dermatol. 2013 Jan;149(1):79-83. doi: 10.1001/2013.jamadermatol.548.

Abstract

Background: Neutrophilic dermatoses comprise a wide spectrum of inflammatory diseases with overlapping features characterized histologically by the presence of an aseptic neutrophilic infiltrate in the epidermis, dermis, and/or hypodermis and are often associated with systemic inflammatory and neoplastic disorders.

Observations: We describe 3 patients with an unusual neutrophilic dermatosis characterized by relapsing episodes of fever, widespread infiltrated plaques with bullous appearance, and variable involvement of the arms, legs, abdomen, and/or trunk. Light microscopy studies showed marked edema of the papillary dermis with an inflammatory infiltrate consisting mainly of mature neutrophils. All 3 patients were morbidly obese, and workup revealed underlying cancer in 2 cases: myeloma and breast carcinoma. Management of the underlying disease resulted in long-term remission of the skin disease.

Conclusions: The clinicopathologic features in our 3 cases best correspond to a widespread giant cellulitis-like form of Sweet syndrome. Knowledge of this newly observed unusual variant of Sweet syndrome within the broad spectrum of neutrophilic diseases is important for its prompt and proper management.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Breast Neoplasms / complications*
  • Breast Neoplasms / pathology
  • Breast Neoplasms / therapy
  • Cellulitis / pathology
  • Female
  • Follow-Up Studies
  • Humans
  • Male
  • Microscopy
  • Middle Aged
  • Multiple Myeloma / complications*
  • Multiple Myeloma / pathology
  • Multiple Myeloma / therapy
  • Obesity, Morbid / physiopathology*
  • Remission Induction / methods
  • Sweet Syndrome / etiology
  • Sweet Syndrome / pathology*