Coincidence of total anomalous pulmonary venous drainage to the superior vena cava, common atrium, and single ventricle: a very rare condition

Echocardiography. 2013 Apr;30(4):E98-101. doi: 10.1111/echo.12141. Epub 2013 Jan 30.


Single ventricle defects, including inflow emptying into 1 ventricle, occur at an incidence of 0.05-0.1 per 10,000 live births. The association of total anomalous pulmonary venous drainage (TAPVD) with single ventricle defects is a risk factor for poor outcome. Conversely, common atrium, a rare congenital anomaly, is an endocardial cushion defect. We present a rare case of an unoperated patient with coincidence of a single ventricle defect, TAPVD with direct drainage from the pulmonary veins into the superior vena cava, and common atrium. To the best of our knowledge, such a case has not been previously reported in the literature.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / diagnostic imaging*
  • Adult
  • Diagnosis, Differential
  • Heart Atria / abnormalities
  • Heart Atria / diagnostic imaging*
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Humans
  • Male
  • Pulmonary Artery / abnormalities*
  • Pulmonary Artery / diagnostic imaging
  • Rare Diseases / diagnostic imaging
  • Ultrasonography
  • Vena Cava, Superior / abnormalities*
  • Vena Cava, Superior / diagnostic imaging