Glaucoma and expulsive hemorrhage mechanisms in the Sturge-Weber syndrome

Ophthalmology. 1979 Jul;86(7):1360-6. doi: 10.1016/s0161-6420(79)35391-x.

Abstract

An eye from an adult with Sturge-Weber syndrome and glaucoma is described histologically following enucleation for massive choroidal hemorrhage. The specimen is noted to contain hemangiomas of the episclera and choroid as well as a partial angle cleavage abnormality. Histologic evidence reviewed herein supports the concept that infantile glaucoma associated with this syndrome may be associated with marked filtration angle cleavage deformities. Some Sturge-Weber patients who develop unilateral glaucoma later as juveniles or adults appear to have milder expressions of angle cleavage abnormality or a forme fruste of this angle disorder. Any surgical procedure for this glaucoma preferably should be one which minimizes or eliminates operative hypotony, thus avoiding a possible expulsive hemorrhage.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Choroid Hemorrhage / pathology*
  • Choroid Neoplasms / pathology
  • Eye Enucleation
  • Glaucoma / pathology*
  • Hemangioma, Cavernous / pathology
  • Humans
  • Male
  • Scleral Diseases / pathology
  • Sturge-Weber Syndrome / pathology*