Congenital portosystemic venous shunt in a preterm Rh-isoimmunized infant

Indian J Pediatr. 2013 Dec;80(12):1053-5. doi: 10.1007/s12098-013-0972-4. Epub 2013 Feb 7.


The authors report a preterm infant with Rh-isoimmunization, who had persistent hepato-splenomegaly with conjugated hyperbilirubinemia, transaminitis, and hyperammonemia. Ultrasound abdomen revealed an intrahepatic portosystemic venous shunt (PSVS). The child was managed conservatively. On follow up at 2.4 y of age, the child is having normal growth and development, but with persisting shunt. Severe Rh-isoimmunisation in a neonate can sometimes share some of the features of congenital PSVS and delay the diagnosis of the latter. The index case had shunt ratio >80 % during the neonatal period but did not require any intervention.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Humans
  • Infant, Premature*
  • Male
  • Portal Vein / abnormalities*
  • Portal Vein / diagnostic imaging
  • Rh Isoimmunization*
  • Ultrasonography
  • Vascular Malformations* / complications
  • Vascular Malformations* / diagnostic imaging

Supplementary concepts

  • Patent Ductus Venosus