[Dilatation treatment of esophageal stenoses in young patients with recessive epidermolysis bullosa dystrophica]

Z Gastroenterol. 1990 Mar;28(3):157-9.
[Article in German]

Abstract

Recessive dystrophic epidermolysis bullosa is a hereditary disorder affecting both skin and esophageal mucosa. The esophagus is frequently affected resulting in almost complete obstruction. We report here the use of inflatable dilatator balloons as a new treatment of esophageal stenosis in three young patients. Dilatation therapy was tolerated well in all three cases and lead to a long standing success. The patients lived without complaints and they did eat normally up to 2.5 years following dilatation.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adolescent
  • Adult
  • Catheterization / instrumentation
  • Catheterization / methods*
  • Combined Modality Therapy
  • Epidermolysis Bullosa / genetics*
  • Epidermolysis Bullosa / therapy
  • Esophageal Stenosis / genetics*
  • Esophageal Stenosis / therapy
  • Female
  • Humans
  • Male
  • Phenytoin / administration & dosage

Substances

  • Phenytoin