Beta-ketothiolase deficiency and pregnancy

Int J Obstet Anesth. 2013 Jul;22(3):260-1. doi: 10.1016/j.ijoa.2013.03.006. Epub 2013 May 9.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Acetyl-CoA C-Acyltransferase / deficiency*
  • Acetyl-CoA C-Acyltransferase / genetics
  • Adult
  • Amino Acid Metabolism, Inborn Errors / genetics*
  • Amino Acid Metabolism, Inborn Errors / therapy*
  • Anesthesia, Obstetrical
  • Anesthesia, Spinal
  • Bradycardia / therapy
  • Cesarean Section / methods
  • Female
  • Fetal Distress / therapy
  • Humans
  • Infant, Newborn
  • Ketone Bodies / metabolism
  • Ketosis / etiology
  • Monitoring, Physiologic
  • Patient Care Planning
  • Pregnancy
  • Pregnancy Complications / therapy*

Substances

  • Ketone Bodies
  • Acetyl-CoA C-Acyltransferase

Supplementary concepts

  • Beta ketothiolase deficiency