Palmoplantar contractures in childhood: a rare complication of vascular Ehlers-Danlos syndrome

Clin Exp Dermatol. 2013 Jul;38(5):517-9. doi: 10.1111/ced.12064. Epub 2013 May 15.


Although catastrophic vascular complications in vascular Ehlers-Danlos Syndrome (EDS) are well recognized, other complications such as flexion contractures and tendon nodules are rarely reported and poorly characterized. We report a young man with vascular EDS, who developed flexion contractures and tendon nodules, causing considerable disability. Limited management strategies are available for these complications, which have continued to prove a challenge to management.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Contracture / etiology*
  • Ehlers-Danlos Syndrome / complications*
  • Foot Deformities, Acquired / etiology*
  • Hand Deformities, Acquired / etiology*
  • Humans
  • Male