Double-chambered right ventricle: a review

Cardiovasc Pathol. 2013 Nov-Dec;22(6):417-23. doi: 10.1016/j.carpath.2013.03.004. Epub 2013 May 20.


A double-chambered right ventricle is a rare heart defect in which the right ventricle is separated into a high-pressure proximal and low-pressure distal chamber. This defect is considered to be congenital and typically presents in infancy or childhood but has been reported to present rarely in adults. It can be caused by the presence of anomalous muscle tissue, hypertrophy of the endogenous trabecular bands, or an aberrant moderator band; all of which will typically result in progressive obstruction of the outflow tract. In this paper, we will discuss the general anatomy of the right ventricle, the relevant embryology of the heart, and the presentation, diagnosis, and treatment of a double-chambered right ventricle.

Keywords: Anomalous muscle band; Congenital heart disease; Crista supraventricularis; Heart defect; Moderator band; Septoparietal trabeculations; Subinfundibular pulmonary stenosis.

Publication types

  • Review

MeSH terms

  • Coronary Angiography
  • Disease Progression
  • Echocardiography, Doppler, Color
  • Heart Defects, Congenital / complications
  • Heart Defects, Congenital / pathology*
  • Heart Defects, Congenital / physiopathology
  • Heart Defects, Congenital / therapy
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / physiopathology
  • Heart Ventricles / surgery
  • Humans
  • Hypertrophy
  • Magnetic Resonance Imaging
  • Predictive Value of Tests
  • Prognosis
  • Ventricular Function, Right
  • Ventricular Outflow Obstruction / etiology
  • Ventricular Pressure