Background: Intracranial arteriovenous malformation rarely causes pulmonary hypertension and congestive heart failure in the newborn. Its diagnosis is challenging because cardiomegaly may suggest an intra-cardiac structural lesion.
Case presentation: We present two newborns, one 2-day-old male and the other 11-day-old female, with intracranial arteriovenous malformation and misdiagnosis of congenital heart disease.
Conclusion: Precise echocardiography revealed the secondary signs of cranial arteriovenous malformation and had the major role in early diagnosis.
Keywords: Congestive heart failure; Dilated brachiocephalic arteries; Doppler echocardiography.