Guidelines for the diagnosis and treatment of idiopathic pulmonary fibrosis. Sociedad Española de Neumología y Cirugía Torácica (SEPAR) Research Group on Diffuse Pulmonary Diseases
Arch Bronconeumol. 2013 Aug;49(8):343-53.
doi: 10.1016/j.arbres.2013.03.011.
Epub 2013 Jun 4.
[Article in
English,
Spanish]
Affiliation
- 1 Servicio de Neumología, Hospital Clínic, Barcelona, España. axaubet@clinic.ub.es
Abstract
Idiopathic pulmonary fibrosis is defined as a chronic fibrosing interstitial pneumonia limited to the lung, of unknown cause, with poor prognosis and few treatment options. In recent years there has been an increase in their prevalence, probably due to the optimization of diagnostic methods and increased life expectancy. The ATS/ERS Consensus (2000) established the diagnostic criteria and recommendations for the assessment of the disease course and treatment. Later studies have helped to redefine diagnostic criteria and treatment options. In 2011, an international consensus was published, establishing diagnostic criteria and new treatment strategies. These guidelines have been updated with the newest aspects of diagnosis and treatment of idiopathic pulmonary fibrosis. A level of evidence has been identified for the most relevant questions, particularly with regard to treatment options.
Keywords:
Diagnosis; Diagnóstico; Fibrosis pulmonar idiopática; Idiopathic pulmonary fibrosis; Tratamiento; Treatment.
Copyright © 2012 SEPAR. Published by Elsevier Espana. All rights reserved.
Publication types
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Practice Guideline
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Research Support, Non-U.S. Gov't
MeSH terms
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Acetylcysteine / therapeutic use
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Biopsy
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Bronchoalveolar Lavage Fluid
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Cell- and Tissue-Based Therapy
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Clinical Trials as Topic
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Contraindications
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Diagnostic Imaging
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Disease Progression
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Evidence-Based Medicine
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Gastroesophageal Reflux / complications
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Genetic Therapy
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Glucocorticoids / therapeutic use
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Humans
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Hypertension, Pulmonary / etiology
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Idiopathic Pulmonary Fibrosis / diagnosis*
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Idiopathic Pulmonary Fibrosis / epidemiology
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Idiopathic Pulmonary Fibrosis / etiology
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Idiopathic Pulmonary Fibrosis / pathology
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Idiopathic Pulmonary Fibrosis / therapy*
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Immunologic Factors / therapeutic use
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Incidence
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Indoles / therapeutic use
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Lung / pathology
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Lung Transplantation
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Oxygen Inhalation Therapy
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Palliative Care
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Prevalence
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Prognosis
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Pulmonary Emphysema / etiology
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Pyridones / therapeutic use
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Risk Factors
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Spain / epidemiology
Substances
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Glucocorticoids
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Immunologic Factors
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Indoles
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Pyridones
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pirfenidone
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nintedanib
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Acetylcysteine