Ventricular arrhythmias due to left ventricular noncompaction cardiomyopathy: a diagnosis in hindsight

Heart Lung Circ. 2014 Feb;23(2):e67-8. doi: 10.1016/j.hlc.2013.05.645. Epub 2013 Jun 21.

Abstract

Left ventricular noncompaction cardiomyopathy is a rare congenital cardiomyopathy which predisposes to sudden cardiac death. We describe the case of a 24 year-old man who had previously received an implantable cardioverter-defibrillator for sustained ventricular tachycardia and was later diagnosed with left ventricular noncompaction cardiomyopathy during a hospitalisation for device infection.

Keywords: Arrhythmia; Cardiac MRI; Dilated cardiomyopathy; Implantable cardioverter-defibrillator; Left ventricular noncompaction cardiomyopathy; Ventricular tachycardia.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Arrhythmias, Cardiac* / diagnosis
  • Arrhythmias, Cardiac* / etiology
  • Arrhythmias, Cardiac* / pathology
  • Cardiomyopathies* / diagnosis
  • Cardiomyopathies* / etiology
  • Cardiomyopathies* / pathology
  • Defibrillators, Implantable / adverse effects*
  • Heart Ventricles / pathology*
  • Humans
  • Male
  • Tachycardia, Ventricular / therapy