Right pulmonary artery to left atrial fistula: a rare presentation

World J Pediatr Congenit Heart Surg. 2012 Jul 1;3(3):382-4. doi: 10.1177/2150135112438233.


Right pulmonary artery to left atrial fistula is a rare congenital vascular anomaly which usually presents with cyanosis, clubbing, dyspnea, and signs and symptoms of a right to left shunt. Paradoxical embolism to the brain resulting in cerebral abscess formation and death is a rare and ominous complication that has been described. We describe an unusual presentation with abdominal pain resulting from splenic infarction.

Keywords: congenital heart disease (CHD); congenital heart surgery; fistula; pulmonary arteries.