Dentin dysplasia type I

BMJ Case Rep. 2013 Jun 27:2013:bcr2013009403. doi: 10.1136/bcr-2013-009403.


Dentin dysplasia type I is a rare hereditary disturbance of dentin formation characterised clinically by nearly normal appearing crowns and hypermobility of teeth that affects one in every 100,000 individuals and manifests in both primary and permanent dentitions. Radiographic analysis shows obliteration of all pulp chambers, short, blunted, and malformed roots, and periapical radiolucencies of non-carious teeth. This paper presents three cases demonstrating classic features of type I dentin dysplasia.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Child
  • Dentin Dysplasia / diagnosis*
  • Female
  • Humans
  • Male

Supplementary concepts

  • Dentin dysplasia, type 1