Thoraco-omphalopagus asymmetric conjoined twins: report of a case and complete review of the literature

J Plast Reconstr Aesthet Surg. 2014 Jan;67(1):e18-21. doi: 10.1016/j.bjps.2013.06.022. Epub 2013 Jul 1.

Abstract

Thoraco-omphalopagus asymmetric conjoined twinning is a rare condition in which a grossly defective foetus (the parasite) is attached to the thorax and upper abdomen of the main foetus (the autosite). We describe a case of thoraco-omphalopagus asymmetric conjoined twins in which the autosite had an associated large-diameter omphalocoele that was successfully separated at our institution. Reconstruction of the resulting abdominal-wall defect was performed using a flap from the gluteal region and the proximal portion of the inferior limb of the parasite, which is demonstrated. In addition, a review of all previously published cases is presented, showing that overall positive results can be obtained in treating this condition and that the presence and degree of cardiac involvement have a major influence on the prognosis.

Keywords: Congenital defects; Conjoined twins; Omphalocoele; Reconstructive surgical procedure; Surgical flap.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Abdominal Wall / surgery*
  • Hernia, Umbilical / surgery*
  • Humans
  • Infant, Newborn
  • Male
  • Plastic Surgery Procedures / methods*
  • Surgical Flaps
  • Thoracic Wall / surgery*
  • Twins, Conjoined / surgery*