Unilateral duplication of the cerebellar hemisphere and internal, middle, and external ear: a clinical case study

Plast Reconstr Surg. 1990 Sep;86(3):550-3. doi: 10.1097/00006534-199009000-00028.


This article presents the unique congenital anomaly complex of ipsilateral cerebellar hemisphere duplication and internal, middle, and external ear duplication. Diagnostic techniques included a head CT scan, a three-dimensional head CT scan, and a head MRI. An aberrant notochordal split was proposed as the embryologic mechanism leading to the development of such anomalies.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / diagnosis
  • Abnormalities, Multiple / embryology*
  • Cerebellum / abnormalities*
  • Child
  • Ear / abnormalities*
  • Ear, External / abnormalities
  • Ear, Inner / abnormalities
  • Ear, Middle / abnormalities
  • Humans
  • Male