Transcatheter aortic valve implantation in surgically repaired double outlet right ventricle

Congenit Heart Dis. 2014 Sep-Oct;9(5):E153-7. doi: 10.1111/chd.12114. Epub 2013 Jul 19.


A 52-year-old male patient, with a medical history of surgically repaired double outlet right ventricle presented with severe aortic stenosis (AS) and hepatitis C with cirrhosis, presented with New York Heart Association Class IV heart failure. During evaluation for a liver transplant, he was deemed a poor surgical candidate due to his aortic valve disease and cirrhosis with model for end-stage liver disease score of 14. Transthoracic echocardiogram showed severe AS with a mean gradient of 62 mm Hg and calculated aortic valve area of 0.74 cm(2) with a normal ejection fraction of 65%. The patient underwent transfemoral implantation of a 23-mm Edwards Sapien commercial heart valve with significant mean gradient reduction across the aortic valve from 62 to 13 mm Hg. The patient was observed in the coronary care unit and discharged home 2 days postprocedure with his clinical symptoms greatly improved.

Keywords: Aortic Stenosis; Double Outlet Right Ventricle; TAVI.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Aortic Valve Stenosis / diagnosis
  • Aortic Valve Stenosis / physiopathology
  • Aortic Valve Stenosis / therapy*
  • Aortic Valve* / diagnostic imaging
  • Aortic Valve* / physiopathology
  • Cardiac Catheterization* / instrumentation
  • Double Outlet Right Ventricle / surgery*
  • Echocardiography, Transesophageal
  • Heart Valve Prosthesis
  • Heart Valve Prosthesis Implantation / instrumentation
  • Heart Valve Prosthesis Implantation / methods*
  • Hemodynamics
  • Humans
  • Male
  • Middle Aged
  • Prosthesis Design
  • Recovery of Function
  • Severity of Illness Index
  • Time Factors
  • Treatment Outcome