Rehabilitation of medically complex ectodermal dysplasia with novel surgical and prosthodontic protocols

Int J Oral Maxillofac Surg. 2014 Mar;43(3):301-4. doi: 10.1016/j.ijom.2013.08.004. Epub 2013 Sep 12.


The functional and aesthetic needs of a 17-year-old patient afflicted with ectodermal dysplasia, chronic long-term immunosuppression, cleft palate, velopharyngeal insufficiency, hypernasality, maxillary hypoplasia, and oligodontia were met with a multidisciplinary team approach. Predictable functional and aesthetic outcomes were obtained with a combination of injection augmentation of the soft palate and nasopharynx and rigid fixation maxillary external distraction with immediate placement and immediate load protocols. No biological or prosthetic complications were noted after definitive rehabilitation with a mandibular implant-retained fixed prosthesis and a maxillary implant-retained detachable prosthesis.

Keywords: chronic immune suppression; cleft palate; distraction osteogenesis; ectodermal dysplasia; immediate implant load; immediate implant placement; maxillary hypoplasia; oligodontia; treatment outcome; young adult.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Cephalometry
  • Dental Implantation, Endosseous / methods*
  • Dental Prosthesis, Implant-Supported*
  • Ectodermal Dysplasia / diagnostic imaging
  • Ectodermal Dysplasia / surgery*
  • Esthetics
  • Humans
  • Male
  • Mandible / abnormalities*
  • Mandible / diagnostic imaging
  • Mandible / surgery
  • Maxilla / abnormalities*
  • Maxilla / diagnostic imaging
  • Maxilla / surgery
  • Radiography